Tufted Angioma Associated with Kasabach-Merritt Phenomenon: A Therapeutic Challenge

Tufted angioma associated with Kasabach-Merritt phenomenon: a therapeutic challenge.

Fig. 1. (A) Tufted angioma involving the chin in a one-month-old child. (B) The patient at 2 months of age showing a subtle increase in tumour size and decrease in platelet count. (C) A subtle residual lesion on the chin of the patient at the age of 5 years. Tufted angioma (TA) is an infrequently seen, benign vascular tumour, which was first described in 1949 (1). It is characterized clinically...

Intractable Tufted Angioma Associated with Kasabach-Merritt Syndrome

Received May 11, 2012, Revised June 14, 2012, Accepted for publication July 12, 2012 *These authors are contributed equally to this work. Corresponding author: Kyoung Chan Park, Department of Dermatology, Seoul National University Bundang Hospital, 82 Gumi-ro 173beon-gil, Bundang-gu, Seongnam 463-707, Korea. TEL: 82-31-787-7311, Fax: 82-31-787-4058, E-mail: [email protected] This is an Open Acce...

Efficiency of an mTOR Inhibitor in Kasabach-Merritt Phenomenon with Indolent Tufted Angioma: A Case Report.

Kasabach-merritt syndrome arising from tufted angioma successfully treated with systemic corticosteroid.

We report a case of Kasabach-Merritt syndrome arising from a tufted angioma successfully treated with systemic corticosteroid. A 2-month-old male infant presented with a palm-sized, erythematous induration on his left pubis. The lesion was diagnosed as tufted angioma histopathologically. After 1 month, the lesion suddenly expanded to the abdomen and scrotum. Initial laboratory tests were consis...

[Kaposiform haemangioendothelioma with Kasabach-Merritt phenomenon].

Kasabach-Merritt phenomenon is a serious coagulopathy associated with kaposiform hemangioendothelioma (KHE), tufted angioma, and possibly other vascular neoplasms. KHE presenting in the absence of Kasabach-Merritt phenomenon is rare, although tufted angioma frequently occurs without thrombocytopenia. We retrospectively reviewed 10 cases of KHE without Kasabach-Merritt phenomenon. The tumors app...